000K  utf8
1100  2022$c2022-01-12
1500  eng
2050  urn:nbn:de:hbz:465-20220805-123638-6
2051  10.3390/jcm11020366
3000  Dinger, Thiemo Florin
3010  Blau, Tobias
3010  Chihi, Mehdi
3010  Darkwah Oppong, Marvin
3010  Deuschl, Cornelius
3010  Eerikäinen, Maija Susanna
3010  Gembruch, Oliver
3010  Jabbarli, Ramazan
3010  Michel, Anna
3010  Pierscianek, Daniela
3010  Sure, Ulrich
3010  Uerschels, Anne-Kathrin
3010  Wrede, Karsten Henning
4000  New Subform? Fast-Progressing, Severe Neurological Deterioration Caused by Spinal Epidural Lipomatosis  [Dinger, Thiemo Florin]
4209  Spinal epidural lipomatosis (SEL) is a rare condition caused by hypertrophic growth of epidural fat. The prevalence of SEL in the Western world is approximately 1 in 40 patients and is likely to increase due to current medical and socio-economic developments. Rarely, SEL can lead to rapid severe neurological deterioration. The pathophysiology, optimal treatment, and outcome of these patients remain unclear. This study aims to widen current knowledge about this "SEL subform" and to improve its clinical management. A systematic literature review according to the PRISMA guidelines using PubMed, Scopus, Web of Science, and Cochrane Library was used to identify publications before 7 November 2021 reporting on acute/rapidly progressing, severe SEL. The final analysis comprised 12 patients with acute, severe SEL. The majority of the patients were male (9/12) and multimorbid (10/12). SEL mainly affected the thoracic part of the spinal cord (11/12), extending a median number of 7 spinal levels (range: 4-19). Surgery was the only chosen therapy (11/12), except for one critically ill patient. Regarding the outcome, half of the patients regained independence (6/11; = modified McCormick Scale ≤ II). Acute, severe SEL is a rare condition, mainly affecting multimorbid patients. The prognosis is poor in nearly 50% of the patients, even with maximum therapy. Further research is needed to stratify patients for conservative or surgical treatment.
4950  https://doi.org/10.3390/jcm11020366$xR$3Volltext$534
4950  https://nbn-resolving.org/urn:nbn:de:hbz:465-20220805-123638-6$xR$3Volltext$534
4961  https://duepublico2.uni-due.de/receive/duepublico_mods_00076420
5051  610
5550  acute paraparesis
5550  atypical fat depositions
5550  neurological outcome
5550  pathophysiology
5550  spinal cord injury
5550  spinal epidural lipomatosis
5550  spinal surgery
5550  spine